3. CVOs
60% asymptomatic.
The most common symptoms ,, syncope and rhythm disturbances (43%)
,,,, chest pain (39%) and embolic events (2%).
Some apical outpouchings may resemble a Takotsubo cardiomyopathy
,,,,,, The clinical setting and the reversibility of the dyskinesia are the main
diagnostic features.
4.
5. 1) Myocardial crypts and clefts
Narrow, deep invaginations within the myocardium >>> disarray of the
myocardial fibers.
Fissures = crevices = recesses =crypts= clefts.
Recess is the smallest one <50% of the myocardial thickness , the cleft used
when u deal with HCM.
Crypts , Crevices, Fissures & Clefts >50% of the myocardial thickness
Location : Basal posterior septum and LV-free wall.
Def in CMRI:
A) V- or U-shaped extension of blood signal in cines >50% of the thickness of
the adjoining compact myocardium in diastole, Never exceeds the pericardial
margin.
B) Narrowing /obliteration in systole.
C)No segmental contractility defects.
6. partial crypts or recesses < 25%–50% of the wall thickness,,,, no clinical
significance.
“Cleft” used in HCM >> narrow invaginations within the left ventricular
myocardium.
Cleft in HCM
7. 2)Diverticulum & Congenital Ventricular Diverticulum
(CVD)
Described for the first time by O’Bryan in 1838.
A)finger-like protrusion from the internal cavity extending outside the epicardium.
B)Narrow neck .
Diameter from 0.5 to 9 cm.
May be multiple = ventricular diverticulosis.
Apex and perivalvular area, never been found in the IVS.
Types : muscular or fibrous.
Fibrous diverticulum =pseudodiverticulum.
Progressive enlargement and spontaneous rupture of a diverticulum have been
described.
8. CVD isolated or associated with midline thoraco-abdominal congenital
abnormalities. CVD as part of a complex
associations Include:
(1) median line abdominal wall defects (omphalocele) .
(2) inferior sternal defects (aplasia and cleft sternum).
(3) anterior diaphragmatic defects.
(4) diaphragmatic pericardium defects (absence of the inferolateral
pericardium).
(5) complex cardiac abnormalities.