Congenital ear disorders

2. Congenital abnormalities are the products
of error in embryogenesis or the result of
intrauterine event that affect embryonic
and fetal growth.
The arrest of development may result in
various deformity.

3.  Anotia
 Microtia
 Macrotia
 Accessory auricles
 Preauricular sinuses
 Darwin’s tuburcules
 Wildermuth’s ear

4.  Ear canal stenosis
 Aural atresia
 Ossicular deformities
 Mandibulofacial dystosis

5. ANOTIA
A rare, congenital deformity involves complete
absence of auricle or Pinna.
Causes are defect in gene or taking isotretinoin
during pregnancy.
Treatment is cosmetic reconstruction of the
external ear’s normal shape and repair of ear
canal.

6. ANOTIA

7. MICROTIA
Here Pinna or external ear is
underdeveloped.
Treatment is prosthetic ear or
ear reconstruction surgery.

9. MICROTIA
It is a congenital ear deformity
marked by excessive growth of ear.
Causes are inherited genetic
disorders.
Otoplasty is performed to reduce the
size.

11. ACCESSORY AURICLES
Polyotia is extreme rare congenital anomaly
It is defined as an accessory ear that is large
enough to resemble an additional Pinna.
Treatment is surgical excision.

12. POLYOTIA

13. PREAURICULAR SINUS
Also known as congenital auricular fistula or
Preauricular cysts.
It is a common birth defect marked by nodule,
dimple located adjacent to the external ear.
Treatment are systemic antibiotics for
infection and surgery to remove sinus.

15. DARWIN’S TUBERCLE
 It is a congenital ear condition often presents
as a thickening on the helix of the ear at the
junction of the upper and middle thirds.

16. WILDERMUTH’S EAR
Congenital anomalies helix is
turned backward and the
anthelix is prominent.
Treatment is Otoplasty.

18. EAR CANAL STENOSIS
 Narrowing of ear canal develops
when ear canal fails to develop
during 7th month in uterus.
 It is repaired by widening the canal
by canalpalsty.

20. AURAL ATRESIA
 Absence or incomplete formation of an
external ear canal.

21. OSSICULAR DEFORMITIES
 Malleus is the most frequent
malformed ossicles.

22. MANDIBULOFACIAL DYSTOSIS
 Hypoplasia of the middle third of
face.
 Hypoplasia of mandible and
underdevelopment of ear.
 Also known as Treacher Collins
syndrome.

23. TREACHER COLLINS SYNDROME