PRESENTATION ON THE VARIOUS CONGENITAL CAUSESS OF HEARING LOSS AND RESPECTIVE IMAGING, MS OTOLARYNGOLOGY ACME PARIYARAM MEDICAL COLLEGE

11. Advantage : Combination of high signal levels and
extremely high spatial resolution.

13. Otic Placode

14. Otic Pit

15. OTOCYST
DORSAL
POUCH
UTRICLE
SCC
VENTRAL
POUCH
COCHLEAR
DUCT
SACCULE

24. SENNAROGLU
SAATCI
classification

29. HRCT shows small left internal auditory canal (black arrow) and absence of the entire
vestibulo-cochlear structures (white arrow), consistent with Michel deformity

30. Oblique sagittal 3D-FIESTA sequence, through the small internal auditory canal shows thinned-out
eighth nerve (block back arrow), with no divisions and normal facial nerve antero-superiorly (arrow)

32. DD: LABYRINTHITIS
OSSIFICANS

34. absence of cochlear nervemalformed LSCC
Dialated IAC

36. FIGURE EIGHT

38. stenotic IAC
only a basal turn

52. CT: The opening for vestibular aqueduct is enlarged. The cochlea is dysplastic
with fusion of its middle and apical turns.
MRI: Axial CISS image shows enlarged endolymphatic sac with high T2 signal.

53. MRI: T2 axial image shows enlarged aqueducts (white arrows) and a very
large right sac. The cochleas are dysplastic..

54. MRI: Axial CISS image demonstrates markedly enlarged
enolymphatic sacs bilaterally.

61. Oblique sagittal - shows the facial and
vestibular nerves in their normal
location, with the cochlear nerve barely
or almost not seen in the anteroinferior
quadrant.

65. (a)Axial T2- weighted MR image obtained in a child with
complete labyrinthine aplasia shows an arachnoid cyst.
(b) Axial T2-weighted MR image obtained in another child
with congenital SNHL shows focal white matter signal
abnormalities

82. BILATERAL SSCD
• Reformatted sagittal- oblique CT image
through the left semicircular canal shows
full size of the dehiscence.

85. • middle ear soft tissue with ossicular destruction
• soft tissue in mastoid with erosion of bony septae

87. COCHLEAR OTOSPONGIOSIS. CT: Coronal and axial images demonstrate diffuse demineralization
of the otic capsule.

88. MRI: T1 axial and coronal post-contrast images demonstrate abnormal signal in the otic capsule